pleuropulmonary blastoma in children: a case report

نویسندگان

azamsadat hashemi hematology, oncology and genetic research center, shahid sadoughi university of medical sciences, yazd, iran

azadeh souzani hematology, oncology and genetic research center, shahid sadoughi university of medical sciences, yazd, iran

amineh souzani hematology, oncology and genetic research center, shahid sadoughi university of medical sciences, yazd, iran

sara keshavarzi hematology, oncology and genetic research center, shahid sadoughi university of medical sciences, yazd, iran

چکیده

pleuropulmonary blastoma [ppb] is a very rare, highly aggressive and malignant tumor that originates from either the lungs or pleura. it occurs mainly in children aged less than five or six years. it has poor prognosis with three different subtypes: cystic [type i], combined cystic and solid [type ii] and solid [type iii]. ppb is treated with aggressive multimodal therapies including surgery and chemotherapy. we present a case of 3.5 years old boy with ppb type ii successfully treated with complete surgical resection followed by neoadjuvant chemotherapy.

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عنوان ژورنال:
iranian journal of cancer prevention

جلد ۵، شماره ۲، صفحات ۱۰۵-۱۰۷

کلمات کلیدی
[ ' p u l m o n a r y b l a s t o m a ' , ' c h i l d ' , ' n e o p l a s m s p l e a s e c i t e t h i s a r t i c l e a s ' , ' h a s h e m i a ' , ' s o u z a n i a ' , ' s o u z a n i a ' , ' k e s h a v a r z i s . p l e u r o p u l m o n a r y b l a s t o m a i n c h i l d r e n ' , ' a c a s e r e p o r t . i r a n j c a n c e r p r e v . 2 0 1 2 ' , ' 5 ( 2 ) ' , 1 0 5 , ' 7 . r e f e r e n c e s 1 . c a l a b r i a r ' , ' s r i k a n t h m s ' , ' c h a m b e r l i n k ' , ' b l o c h j ' , ' a t k i n s o n j b . m a n a g e m e n t o f p u l m o n a r y b l a s t o m a i n c h i l d r e n . a m s u r g . 1 9 9 3 ' , 5 9 , 1 9 2 , ' 6 . 2 . w r i g h t j r . p l e u r o p u l m o n a r y b l a s t o m a . a c a s e r e p o r t d o c u m e n t i n g t r a n s i t i o n f r o m t y p e i [ c y s t i c ] t o t y p e i i i [ s o l i d ] . c a n c e r . 2 0 0 0 ' , 8 8 , 2 8 5 3 , ' 8 . 3 . d e h n e r l p ' , ' w a t t e r s o n j ' , ' p r i e s t j . p l e u r o p u l m o n a r y b l a s t o m a ' , ' a u n i q u e i n t r a t h o r a c i c ' , ' p u l m o n a r y n e o p l a s m o f c h i l d h o o d . p e r s p e c t p e d i a t r p a t h o l . 1 9 9 5 ' , 1 8 , 2 1 4 , ' 2 6 . 4 . p r i e s t j r ' , ' m c d e r m o t t m b ' , ' b h a t i a s ' , ' w a t t e r s o n j ' , ' m a n i v e l j c ' , ' d e h n e r l p ' , ' e t a l . p l e u r o p u l m o n a r y b l a s t o m a ' , ' a c l i n i c o p a t h o l s t u d y o f 5 0 c a s e s . c a n c e r . 1 9 9 7 ' , 8 0 , 1 4 7 , ' 6 1 . 5 . p i c a u d j c ' , ' l e v r e y h ' , ' b o u i v e r r ' , ' p u i s j p ' , ' l o u i s d ' , ' f r a p p a z d ' , ' e t a l . b i l a t e r a l c y s t i c p l e u r o p u l m o n a r y b l a s t o m a i n e a r l y i n f a n c y . j p e d i a t r . 2 0 0 0 ' , 1 3 6 , 8 3 4 , ' 6 . 6 . m i n i a t i d n ' , ' c h i n t a g u m p a l a m ' , ' l a n g s t o n c ' , ' d i s h o p m k ' , ' o l u t o y e o o ' , ' n u c h t e r n j g ' , ' e t a l . p r e n a t a l p r e s e n t a t i o n a n d o u t c o m e o f c h i l d r e n x a 0 x a 0 w i t h p l e u r o p u l m o n a r y b l a s t o m a . j p e d i a t r s u r g . 2 0 0 6 ' , 4 1 , 6 6 , ' 7 1 . 7 . p r i e s t j r ' , ' w a t t e r s o n j ' , ' s t r o n g l ' , ' h u f f v ' , ' w o o d s w g ' , ' b y r d r l . p l e u r o p u l m o n a r y b l a s t o m a ' , ' a m a r k e r f o r f a m i l i a l d i s e a s e . j p e d i a t r . 1 9 9 6 ' , 1 2 8 , 2 2 0 , ' 4 . 8 . m a n i v e l j c ' , ' p r i e s t j r ' , ' w a t t e r s o n j ' , ' s t e i n e r m ' , ' w o o d s w g ' , ' w i c k m r ' , ' e t a l . p l e u r o p u l m o n a r y b l a s t o m a . t h e s o ' , ' c a l l e d p u l m o n a r y b l a s t o m a i n c h i l d h o o d . c a n c e r . 1 9 8 8 ' , 6 2 , 1 5 1 6 , ' 2 6 . 9 . d e h n e r l p ' , ' w a t t e r s o n j ' , ' p r i e s t j ' , ' p l e u r o p u l m o n a r y b l a s t o m a . a u n i q u e i n t r a t h o r a c i c p u l m o n a r y n e o p l a s m o f c h i l d h o o d . p e r s p e c t p e d i a t r p a t h o l . 1 9 9 5 ' , 1 8 , 2 1 4 , ' 2 6 . 1 0 . w r i g h t j r . p l e u r o p u l m o n a r y b l a s t o m a ' , ' a c a s e r e p o r t d o c u m e n t i n g t r a n s i t i o n f r o m t y p e i [ c y s t i c ] t o t y p e i i i [ s o l i d ] . c a n c e r . 2 0 0 0 ' , ' 8 8 [ 1 2 ] ' , 2 8 5 3 , ' 8 . 1 1 . p r i e s t j r ' , ' m c d e r m o t t m b ' , ' b h a t i a s ' , ' w a t t e r s o n j ' , ' m a n i v e l j c ' , ' d e h n e r l p . p l e u r o p u l m o n a r y b l a s t o m a ' , ' a c l i n i c o p a t h o l o g i c s t u d y o f 5 0 c a s e s . c a n c e r . 1 9 9 7 ' , 8 0 , 1 4 7 , ' 6 1 . 1 2 . v a r g a s s o ' , ' n o s e v ' , ' f l e t c h e r j a ' , ' p e r e z ' , ' a t a y d e a r . g a i n s o f c h r o m o s o m e 8 a r e c o n f i n e d t o m e s e n c h y m a l c o m p o n e n t s i n p l e u r o p u l m o n a r y b l a s t o m a . p e d i a t r d e v p a t h o l . 2 0 0 1 ' , ' 4 [ 5 ] ' , 4 3 4 , ' 4 5 . 1 3 . k e l s e y a m ' , ' m c n a l l y k ' , ' b i r c h j ' , ' m i t c h e l l e l . c a s e o f e x t r a p u l m o n a r y ' , ' p l e u r o ' , ' p u l m o n a r y b l a s t o m a i n a c h i l d ' , ' p a t h o l o g i c a l a n d c y t o g e n e t i c f i n d i n g s . m e d p e d i a t r o n c o l . 1 9 9 7 ' , 2 9 , 6 1 , ' 4 . 1 4 . p a p a g i a n n o p o u l o s k a ' , ' s h e p p a r d m ' , ' b u s h a p ' , ' g o l d s t r a w p . p l e u r o p u l m o n a r y b l a s t o m a ' , ' i s p r o p h y l a c t i c r e s e c t i o n o f c o n g e n i t a l l u n g c y s t s e f f e c t i v e ? a n n t h o r a c s u r g . 2 0 0 1 ' , ' 7 2 [ 2 ] ' , 6 0 4 , ' 6 0 5 . 1 5 . i n d o l f i p ' , ' c a s a l e f ' , ' c a r l i m ' , ' b i s o g n o g ' , ' n i n f o v ' , ' c e c c h e t t o g ' , ' e t a l . p l e u r o p u l m o n a r y b l a s t o m a ' , ' m a n a g e m e n t a n d p r o g n o s i s o f 1 1 c a s e s . c a n c e r . 2 0 0 0 ' , ' 8 9 [ 6 ] ' , 1 3 9 6 , ' 4 0 1 . 1 6 . f u n d a ç o r a p ç ı o ğ l u 1 ' , ' t u b a l i m a n 2 ' , ' g ö r k e m a k s u 3 ' , ' n a g i h a n i ̇ n a n 4 ' , ' m u r a t d e v e c i 1 y e ş i m g ü r b ü z 5 ' , ' s a l i h t o p ç u 2 . a c a s e r e p o r t w i t h t y p e i i p l e u r o p u l m o n a r y b l a s t o m a ' , ' s u c c e s s f u l t r e a t m e n t w i t h s u r g e r y a n d c h e m o t h e r a p y . t h e t u r k i s h j o u r n a l o f p e d i a t r i c s . x a 0 2 0 0 9 ' , 5 1 , 7 8 , ' 8 1 . ' ]

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